Usually congenital
PV stenosis ➔ right ventricular outflow obstruction ➔ ↑ right side pressure ➔ RVH
HF sx
Wide splitting of S2 (prolonged RV systole ➔ later closing of pulmonic valve)
Systolic murmur that doesn't radiate (like AS) ± ejection click
ECHO
Enlarged pulmonary artery on CXR
Balloon pulmonary valvuloplasty transcatheter dilation